ABSTRACT Various congenital abnormalities are described in children undergoing corrective procedures, surgical interventions and emergency surgeries. Seckle syndrome – first described in 1960, is one among them. It is a genetic heterogeneous disorder, inherited as an autosomal recessive process. Usually the child is characterised by disproportionate dwarfism, mental retardation, dysmorphic facial features like a bird with microcephaly (Bird headed syndrome), skeletal abnormalities and micrognathia. Planned surgery in these children for correctable surgical conditions poses challenge to the anaesthesiologist. Intervention for emergency surgeries may present a more difficult anaesthetic management protocol. Successful anaesthetic management of the presenting child is described to highlight the modification, arrangements required for maintenance of airway, tracheal intubation, maintenance of anaesthesia and post-operative pain relief. Micrognathia and floppy epiglottis were the two significant challenges of management in this child. Circumcision by the paediatric surgeon and dental correction (including root canal procedure) by pedodontic surgeon were simultaneously performed lasting 180 minutes.