ABSTRACT : Turner’s syndrome, 45X, is a chromosomal abnormality in which all or part of one of the sex chromosomes is absent or abnormal, seen in 1:2000 live births. It is associated with anatomical and physiological changes which could pose major anaesthetic challenges. The objective of this report is to discuss the anaesthetic management in these patients in order to decrease perioperative complications. We present the perioperative management of a patient with Turner’s syndrome who underwent canal wall down mastoidectomy.

METHODS : A 34 year old woman diagnosed to have Turner’s syndrome with CSOM was scheduled for mastoidectomy with history of hypothyroidism on medication, primary amenorrhoea and hoarseness of voice. On examination she had short stature, bilateral cataract, short neck, restricted neck and TMJ movement. No abnormality detected on systemic examination and indirect laryngoscopy. Laboratory investigations, ECG were within normal limits.

Patient was on continuous pulse oximetry, capnography, ECG, NIBP and temperature monitoring. Difficult intubation cart was kept ready and GA induced with fentanyl propofol and succinylcholine. Conventional intubation was done using a 7mm ETT and fixed at 19 cm. Anaesthesia duration was 4h.

RESULTS : Patient had a stable anaesthetic course, extubation, recovery and was shifted to ward.

CONCLUSIONS : Turner’s syndrome is associated with a myriad of airway, cardiac and endocrinal abnormalities which need meticulous anaesthetic planning, preparedness and monitoring.